Table 1. Distinctive (primary) cutaneous mucinoses 1.
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I. Degenerative–inflammatory mucinoses |
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Dermal |
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1. Lichen myxedematosus (papular mucinosis) |
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· Generalized and sclerodermoid (scleromyxedema) |
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· Localized: discrete type, acral persistent papular mucinosis, cutaneous mucinosis of infancy, nodular type |
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· Atypical forms |
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2. Reticular erythematous mucinosis |
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3. Scleredema |
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4. Dysthyroidotic mucinoses |
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· Localized (pretibial) myxedema |
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· Generalized myxedema |
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5. Papular and nodular mucinosis with connective tissue diseases (lupus erythematosus, dermatomyositis, scleroderma) |
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6. Self-healing cutaneous mucinosis |
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7. Cutaneous focal mucinosis |
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8. Digital mucous cyst |
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9. Miscellaneous mucinoses |
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Follicular |
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1. Pinkus’ follicular mucinosis |
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2. Urticaria-like follicular mucinosis |
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II. Hamartomatous–neoplastic mucinoses |
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1. Mucinous nevus |
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2. (Angio)myxoma |