Table 2. 9 Defining characteristics of Degos [2]

 

 

 

1.

Histologically, Degos is a vasculopathy/endovasculitis

2.

Degos has two variants (a) Benign cutaneous (b) Systemic lethal

3.

An occlusive arteriopathy involves small-caliber vessels

4.

Tissue infarction occurs usually initially involving the skin

5.

Degos initially manifests w/ erythematous, pink/red papules

6.

Papules evolve into papules with porcelain atrophic centers

7.

In the systemic variant GI, brain & organ bleeding kills

8.

Immune, viral, and vascular/hematologic causes are posited

9.

Treatment has no effect on the course of Degos