Table 2. 9 Defining characteristics of Degos [2]
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1. |
Histologically, Degos is a vasculopathy/endovasculitis |
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2. |
Degos has two variants (a) Benign cutaneous (b) Systemic lethal |
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3. |
An occlusive arteriopathy involves small-caliber vessels |
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4. |
Tissue infarction occurs usually initially involving the skin |
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5. |
Degos initially manifests w/ erythematous, pink/red papules |
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6. |
Papules evolve into papules with porcelain atrophic centers |
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7. |
In the systemic variant GI, brain & organ bleeding kills |
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8. |
Immune, viral, and vascular/hematologic causes are posited |
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9. |
Treatment has no effect on the course of Degos |