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Risks of long-term port use in enzyme replacement therapy for lysosomal storage disorders.

  • Author(s): Hendriksz, Christian J
  • Harmatz, Paul
  • Giugliani, Roberto
  • Roberts, Jane
  • Arul, G Suren
  • et al.

Totally implantable vascular access devices (TIVADs) are commonly used in conjunction with enzyme replacement therapy (ERT) for lysosomal storage disorders (LSDs). This case series describes potential complications associated with long-term TIVAD use, such as compromise of skin integrity, infection, or port failures. Best practices and skilled specialists are essential for minimizing complications from long-term TIVAD use for ERT.

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