UCSF

Purpose

To report a case of primary hepatoid adenocarcinoma of the orbit.

Observations

An adult patient was referred for evaluation of an orbital mass. Histopathology of the orbital biopsy indicated a carcinoma with hepatoid features. Laboratory studies revealed normal liver function tests, elevated serum alpha-fetoprotein, and whole-body positron emission tomography/computed tomography scan showed no evidence of liver involvement or an alternative primary origin.

Conclusions and importance

To the authors' knowledge, this is the first reported case of primary hepatoid adenocarcinoma of the orbit.