Dermatology Online Journal
Segmental lesions along blaschko´s lines in an elderly man
- Author(s): Tous Romero, Fátima
- Burillo Martinez, Sara
- Raya-Morales, Carlos
- Gargallo-Moneva, Vanessa
- Maroñas-Jiménez, Lidia
- et al.
Darier disease (DD) is an autosomal dominant genodermatosis characterized by multiple keratotic and crusted papules over seborrheic areas, along with a variable involvement of oral mucosa, palmoplantar region, and nails. Segmental subtypes (type 1 and 2) are uncommon clinically limited forms of DD that usually present at middle age with few cutaneous lesions following Blaschko´s lines. We report a case of extensive multi segmental DD type 1 that developed in an elderly man, an unusual clinical onset of DD that dermatologists should bear in mind.