Syringocystadenocarcinoma papilliferum: a rare tumor with a favorable prognosis
- Author(s): Peterson, Johanna;
- Tefft, Kimberly;
- Blackmon, Joseph;
- Rajpara, Anand;
- Fraga, Garth
- et al.
Published Web Locationhttps://doi.org/10.5070/D3199019620
Syringocystadenocarcinoma papilliferum (SCACP) is a rare adenexal carcinoma with only 21 cases reported in the literature. Most patients describe a long-standing mass with recent change, supporting the idea that SCACP arises from malignant transformation of pre-existing syringocystadenoma papilliferum (SCAP). Syringocystadenocarcinoma papilliferum is generally treated with wide surgical excision of the lesion and patients do exceeding well and require no systemic therapy.