Kommerell diverticulum is the aneurysmal dilatation of the proximal descending aorta at the origin of an aberrant subclavian artery and may occur in either the left-sided or right-sided aortic arch. We report an unusual case of right-sided aortic arch with Kommerell diverticulum and concurrent agenesis of the left common carotid artery in a patient with progressive dysphagia to solid food. A brief overview of embryology, relevant anatomy, radiographic findings, and treatment options of Kommerell diverticulum are presented.