Heterotopic salivary gland tissue consists of otherwise normal salivary tissue, but occurs at a site in which it is normally not present (outside of the major, minor, and accessory salivary glands), with absence of clinical and histological features of branchial cleft anomalies. We herein present a 7-year-old boy with drainage from a small, congenital cystic lesion located at the base of the neck, which was histologically confirmed as salivary gland tissue.