Dermatology Online Journal
Elastosis perforans serpiginosa related to vascular Ehlers-Danlos syndrome
- Author(s): Uldall Pallesen, Kristine Appel
- Lindahl, Kim Hein
- Bygum, Anette
- et al.
Elastosis perforans serpiginosa (EPS) is a rare skin disease with elimination of connective tissue fibers from dermis to epidermis. The typical presentation shows hyperkeratotic red or skin-colored papules arranged in a circinate pattern. We present a 26-year-old woman with EPS known to have vascular Ehlers-Danlos syndrome.